The pulmonary valve in the heart is the valve separating the right ventricle (one of the chambers of the heart) and the pulmonary artery. The pulmonary artery carries oxygen-poor blood to the lungs.
Pulmonary valve stenosis is a rare disorder. In some cases, the problem runs in families. Pulmonary valve stenosis is a heart valve disorder that involves narrowing of the pulmonary valve. This is most often present at birth (congenital). It is caused by a problem that occurs as the baby develops in the womb before birth. The cause is unknown, but genes may play a role. Narrowing that occurs in the valve itself is called pulmonary valve stenosis. There may also be narrowing just before or after the valve. The defect may occur alone or with other heart defects that are present at birth. The condition can be mild or severe.
Some people may need heart surgery to repair or replace the pulmonary valve. The new valve can be made from different materials. If the valve cannot be repaired or replaced, other procedures may be needed.